Resumen. COLLAZO ALVAREZ, Hiralio; TORRECILLA SILVERIO, Dewar; MORALES FLORAT, Jorge Luis y COLLAZO MARIN, Stephens Yecc. Malignant. CASO CLÍNICO. Malignant oropharyngeal fibrous histiocytoma. Resection and radial reconstruction with fasciocutaneous flap. Histiocitoma fibroso maligno de. LETTERS TO THE EDITOR. Malignant fibrous histiocytoma – a rare hepatic tumor . Histiocitoma fibroso maligno, un tumor hepático raro.

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Continuing navigation will be considered mlaigno acceptance of this use. This study supports the results obtained by other authors for MFH in other sites, such as Shinozaki et al.

Malignant fibrous histiocytoma of the head and neck: Services on Demand Journal. Full text is only aviable in PDF. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.

In Vivo, 15pp.

Orphanet: Histiocitoma fibroso maligno

However, other authors like Kearney et al. The tumor was resected with generous margins and the defect was reconstructed with a radial fasciocutaneous flap. Chemotherapy CHT with ifosfamide, trabectedin, dacarbazine, pazopanib have demonstrated efficacy in UPS and are registered and available in most European Union countries. Due to its exceptional location and the implications of this location, we report a new case of malignant fibrous histiocytoma of the soft palate and lateral wall of the oropharynx.

Some immunohistochemical and ultrastructura observations. Sarcomas of the head and neck region. Immediate surgery of a mass without knowledge of its histological nature is strongly discouraged because it is associated with an increased risk of death due to inappropriate resection and increased risk of relapse.

The childhood variant appears have better prognosis. Myxoid fubroso fibrous histiocytoma of the uterus, a case with immunohistochemical, ultrastructural a tumor cell culture studies. Clinical description The tumor arises most commonly during the sixth histiocitona seventh decades of life. Resection and radial reconstruction with fasciocutaneous flap.


Overall, the prognosis is grim where 16 out of the 32 reported patients were dead and in other 8 cases it is not available if the patient died in the course of the disease between 6 days and 34 months median survival: Only 6 cases of malignant fibrous histiocytoma have been reported in the pharynx in the scientific literature. All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Histioocitoma License.

Discussion Since the first report of MFH in by O’Brien and Stout, it has been well recognized as the most common malignant soft tissue tumor. Malignant fibrous histiocytoma is recognized as the most common soft-tissue sarcoma in adults, although its location in the pharynx is unusual.

Hepatic arterial embolization was performed in two cases with no sucess. Histology of biopsy specimen prior to any treatment is crucial to reach diagnosis and shows pleomorphic spindle cell population with large atypical cells frequently exhibiting numerous irregular mitotic figures, associated regions of hemorrhage and necrosis, associated lymphohistiocytic infiltrate and invasion of dermis.

The gross tumor had a gray-colored, fleshy, multilobate appearance. Malignant oropharyngeal fibrous histiocytoma. MFH must be differentiated from other neoplasms that exhibit marked pleomorphism, such as pleomorphic liposarcoma, pleomorphic rhabdomyosarcoma, pleomorphic carcinoma, and leiomyosarcoma. In the myxoid variant, mesenchymal cells are present in a myxoid stroma rich in mucopolysaccharides.

Giant malignant fibrous histiocytoma of the uterus. Abdomen was soft but volumous with positive ascitic wave, tenderness in the right hypocondrium but no distinct hepatomegaly was found. Malignant fibrous histiocytoma MFH represents the most common soft tissue sarcoma histiociotma adults. Prior radiation therapy is a likely risk factor in some cases.

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Prog Obstet Ginecol, 46pp. Patient died 45 days after admission. Anorexia, malaise, fever and weight loss are present in retroperitoneal and inflammatory forms of UPS. The literature on this pathology is reviewed. In 7 cases there was direct invasion of the adjacent organs and in two cases distant metastasis in the lungs and brain.

A 67 year old woman with several years history of clinically non-specific menometrorrhagias and occasional abdominal discomfort. Malignant fibrous histiocytoma of the liver – a case report and review of the literature.

Check this box if you wish to receive a copy of your message. Although the role of irradiation is not well established, different prognostic factors age, sex, tumor location, stage, size, depth, positive surgical margins, irradiation and the dose administered have been analyzed in studies like that of Hsu et al. Soft-tissue sarcomas of the head and neck: Are you a health professional able to prescribe or dispense drugs?

Banhudo Department of Gastroenterology. Malignant fibrous histiocytoma – a rare hepatic tumor. The etiology of the tumor remains unknown.

Arch Otolaryngol Head Surg Neck ; Arch Gynecol Obstet,pp. This type usually is low-grade, with areas of bleeding and hemosiderin deposits, together with a pleomorphic fibrohistiocytic population and high mitotic activity. A population-based epidemiologic and prognostic study of patients. Visceral locations are uncommon and primary hepatic MFH is exceedingly rare.

This type tends to be poorly differentiated and more frequently grade 2 or 3.